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DeCS
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Descriptor English:
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Familial Mediterranean Fever
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Descriptor Spanish:
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Fiebre Mediterránea Familiar
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Descriptor Portuguese:
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Febre Familiar do Mediterrâneo
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Synonyms English:
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Mediterranean Fever, Familial
Periodic Disease
Hereditary Periodic Fever Syndromes
Wolff Periodic Disease
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Tree Number:
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C16.320.306
C20.111.375
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Definition English:
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An autosomal recessive inherited disease characterized by episodic FEVER; severe ABDOMINAL PAIN; PLEURISY; ARTHRITIS; and a characteristic ankle RASH. Disease flare-ups tend to last 3 days, and individuals are asymptomatic between attacks. ORCHITIS; benign recurrent MENINGITIS; HEADACHE; and AMYLOID nephropathy may also occur. (From Medicine (Baltimore) 1998 Jul;77(4):268-97) |
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Indexing Annotation English:
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a specific disease entity: do not use X ref PERIODIC DISEASE for periodically occurring dis ( = PERIODICITY (IM) + disease (IM))
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History Note English:
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2000 (1966)
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Allowable Qualifiers English:
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Record Number:
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10696
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Unique Identifier:
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D010505
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Occurrence in VHL:
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Similar:
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DeCS SciELO LILACS LIS
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